REVEAL Registry Risk Score for Pulmonary Arterial Hypertension (PAH)
Predicts survival in patients with pulmonary arterial hypertension.
When to Use
Associated PAH-connective tissue disease
+1Associated PAH-portopulmonary hypertension
+2Familial PAH
+2Other
0No
0Yes
+1No
0Yes
+2I
-2II
0III
+1IV
+2≥110
0<110
+1≤92
0>92
+1≥440 m
-1165-440 m
0<165 m
+1<50
-250-180
0>180
+1No
0Yes
+1≥80%
-133-79%
0≤32%
+1No
0Yes
+1No
0Yes
+2Result:
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